Thursday, March 29, 2018

Interesting medical tidbits 2

               
                 
Interesting medical tidbits 2
Cardiovascular system
Cyanotic heart diseases

Congestive cardiac failure in Fallots Tetrology is uncommon
Unless associated with
.Pulmonary atrasia
Aortic incompetence
Patent ductus arteriosus
Infective endocarditis
Severe anemia
Endomyocardial fibrosis

 Variants of Fallots tetrology
Acyanotic Fallots(pulmonary stenosis is mild)
Fallots with Pulmonary atresia-clinically no Ejection systolic murmur in pulmonary area but soft continuos murmur below the clavicle or at the back.
Why cyanosis does not occur at birth in Fallots tetrology?
HbF is predominantly in 1st year of life. It binds less avidly to O2 and releases O2 easily at times of need.Hence in first few months (6months) cyanosis is minimal. After 6mths HbF is replaced by HbA which releases O2 less readily.As the child grows up O2 need increase and cyanosis is manifest more.
Cyanotic heart diseases with ischemic lung fields in Xray chest
1.Fallots terology
2.Fallots triology(PS with ASD)
3.Tricuspid atresia(LVH)

Cyanotic Heart disease with plethoric lung fields
1.Transposition of great arteries
2.Peristent truncus arteriosus
3.TAPVD
4.Eisenmengers Syndrome
Chamber hypertrophy in cyanotic heart diseases
cyanotic heart defects  withRight ventricular hypertrophy
TOF
PS with ASD
Transposition
Eisenmengers
TAPVD
cyanotic heart diseases withLeft ventricular hypertrophy
Tricuspid atrasia
(the commonest Cyanotic heart disease with LVH is Tricuspid atrasia)
Biventricular hypertrophy in persistant Truncus arteriosis
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